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Stewart-Treves Syndrome Involving Chronic Lymphedema after Mastectomy of Breast Cancer

Identifieur interne : 000166 ( Main/Exploration ); précédent : 000165; suivant : 000167

Stewart-Treves Syndrome Involving Chronic Lymphedema after Mastectomy of Breast Cancer

Auteurs : Smain Nabil Mesli [Algérie] ; Amin Khayreddine Ghouali [Algérie] ; Fouad Benamara [Algérie] ; Fouzi Ahmed Taleb [Algérie] ; Hicham Tahraoui [Algérie] ; Chakib Abi-Ayad [Algérie]

Source :

RBID : PMC:5322458

Abstract

Steward-Treves syndrome is a cutaneous angiosarcoma that usually appears after long evolution of a lymphoedema after mastectomy for mammary neoplasia associated with an axillary dissection. This is a rare disease develop most of the time in upper arm and often confounded with cutaneous metastasis. Only the biopsy and immunohistochemical study confirm the diagnosis. The treatment is surgical and consists of large cutaneous excision, an amputation of the limb or even its disarticulation and will be followed by chemotherapy. Despite the treatment, the prognosis remains severe with poor survival. We report the case of a patient who had a Steward-Treves syndrome 20 years after lymphoedema following a left mastectomy with axillary dissection.


Url:
DOI: 10.1155/2017/4056459
PubMed: 28280645
PubMed Central: 5322458


Affiliations:


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Le document en format XML

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<p>Steward-Treves syndrome is a cutaneous angiosarcoma that usually appears after long evolution of a lymphoedema after mastectomy for mammary neoplasia associated with an axillary dissection. This is a rare disease develop most of the time in upper arm and often confounded with cutaneous metastasis. Only the biopsy and immunohistochemical study confirm the diagnosis. The treatment is surgical and consists of large cutaneous excision, an amputation of the limb or even its disarticulation and will be followed by chemotherapy. Despite the treatment, the prognosis remains severe with poor survival. We report the case of a patient who had a Steward-Treves syndrome 20 years after lymphoedema following a left mastectomy with axillary dissection.</p>
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<name sortKey="Abi Ayad, Chakib" sort="Abi Ayad, Chakib" uniqKey="Abi Ayad C" first="Chakib" last="Abi-Ayad">Chakib Abi-Ayad</name>
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<name sortKey="Benamara, Fouad" sort="Benamara, Fouad" uniqKey="Benamara F" first="Fouad" last="Benamara">Fouad Benamara</name>
<name sortKey="Ghouali, Amin Khayreddine" sort="Ghouali, Amin Khayreddine" uniqKey="Ghouali A" first="Amin Khayreddine" last="Ghouali">Amin Khayreddine Ghouali</name>
<name sortKey="Ghouali, Amin Khayreddine" sort="Ghouali, Amin Khayreddine" uniqKey="Ghouali A" first="Amin Khayreddine" last="Ghouali">Amin Khayreddine Ghouali</name>
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